Gorham-Stout disease successfully treated with sirolimus (rapamycin): a case report and review of the literature
نویسندگان
چکیده
منابع مشابه
Sirolimus on Gorham-Stout disease. Case report.
BACKGROUND Gorham-Stout disease (GSD) is a rare disease of unknown etiology characterized by vascular proliferation that produces destruction of bone matrix. CASE DESCRIPTION This case is about 43 year old woman who begins with pain in sternum, dyspnea, abdominal mass and, serous-hematic pleural effusion. Imaging tests were performed showing lesions on 6th and 10th left ribs archs. Later, a t...
متن کاملNovel approach of treating Gorham-Stout disease in the humerus--Case report and review of literature.
Gorham-Stout disease or the so-called vanishing bone syndrome is a rare disorder characterized by intra-osseous proliferation of vascular channels resulting in destruction and resorption of the osseous matrix. The exact pathology of this disease showed no evidence of malignant, neuropathic, or infectious components involved in the causation of this disorder except for the culprit of lympho-vasc...
متن کاملFrom tooth extraction to Gorham-Stout disease: A case report
INTRODUCTION Gorham-Stout disease (GSD), or vanishing bone disease, is a very rare condition of unknown aetiology. It is characterised by progressive osteolysis and angiomatosis. CASE PRESENTATION We report the discovery of this very rare disease following a trivial deciduous tooth extraction in a 14-year-old female. We focus initially on the difference between the preoperative orthopantomogr...
متن کاملGorham-Stout syndrome: a case report.
Gorham-Stout syndrome, is an extremely rare disease of the bone, characterized for vascular and lymphatic channels proliferation in bony segments and consequent osseous resorption. There are around 200 cases reported around the world. Although bisphosphonates are used for symptoms relief, there is no standardized treatment established. We present a case that was diagnosed in our centre secondar...
متن کاملA Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement
Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respira...
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ژورنال
عنوان ژورنال: BMC Musculoskeletal Disorders
سال: 2020
ISSN: 1471-2474
DOI: 10.1186/s12891-020-03540-7